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BRIEF REPORT
Year : 2007  |  Volume : 55  |  Issue : 1  |  Page : 55-57

Familial calcific band-shaped keratopathy: Report of two new cases with early recurrence


1 Guru Nanak Eye Centre, University of Delhi, New Delhi - 110 002, India
2 Incharge Division of Genetics and Metabolic Diseases, Dept. of Pediatrics, Lok Nayak Hospital, University of Delhi, New Delhi - 110 002, India
3 Dept. of Pathology, Maulana Azad Medical College and Associated Hospitals, University of Delhi, New Delhi - 110 002, India

Correspondence Address:
Daraius Shroff
E-22A, East of Kailash, New Delhi - 110 065
India
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Source of Support: None, Conflict of Interest: None


DOI: 10.4103/0301-4738.29496

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We report two siblings with the rare entity of familial calcific band-shaped keratopathy (BSK). Detailed ophthalmic and systemic investigations failed to reveal any underlying causative pathology. Topical disodium ethylenediamine-tetraacetate (EDTA) was applied for 30 min to all four eyes. In addition the right eye of the younger sibling required a superficial keratectomy. An improvement in corneal clarity was seen in the immediate postoperative period in both siblings. Histopathology of the keratectomy specimen revealed linear extracellular sub-epithelial granular calcium deposits. However, an early recurrence was noted in all four eyes at four weeks postoperatively. We report the second instance in the English literature of this entity. Band-shaped keratopathy presenting without an obvious etiology merits a complete systemic and ophthalmic workup. Patients with familial idiopathic BSK could be cases with poor prognosis for treatment with EDTA due to an early recurrence of the disease.


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