|LETTER TO THE EDITOR
|Year : 2008 | Volume
| Issue : 4 | Page : 343-344
Vasumathy Vedantham, Jitendra Jethani, Anil Agarwal, Perumalsamy Vijayalakshmi
Aravind Eye Hospital and Postgraduate Institute of Ophthalmology, Madurai, Tamil Nadu, India
|Date of Web Publication||19-Jun-2008|
Consultant, Retina - Vitreous Service, Aravind Eye Hospital and Postgraduate Institute of Ophthalmology, 1, Anna Nagar, Madurai - 625 020, Tamil Nadu
Source of Support: None, Conflict of Interest: None
|How to cite this article:|
Vedantham V, Jethani J, Agarwal A, Vijayalakshmi P. Authors' reply. Indian J Ophthalmol 2008;56:343-4
We thank the reader  for his interest in our article  while we also approach his concerns that inferior oblique overaction can be because of superior oblique dysfunction. However, the very term primary inferior oblique overaction implies that such a possibility has already been excluded. Needless to say our patient underwent a detailed orthoptic workup including measurement of deviation in nine gazes and either head tilt that together with evaluation of duction did not suggest any extraocular muscle dysfunction. The same could not be included in the article because of restrictions in word limit.
We are surprised that the reader should link blepharophimosis to mesodermal dysgenesis and dysfunction of extraocular muscles, no such association has been reported to the best of our knowledge. Further, the eyelids are ectodermally derived and we recommend the reader to refer the book,  which states that the entity of blepharophimosis syndrome is predominantly a dysplasia of the eyelids consisting of inverted inner canthal fold, short palpebral fissure with lateral displacement of inner canthi, low nasal bridge, and ptosis of eyelids with hypoplasia and fibrosis of levator palpebrae superioris.
| References|| |
Pandey PK, Vats P, Kaur N, Kulkarni AG. Primary inferior oblique over action as part of a new syndrome. Indian J Ophthalmol 2008;56:343-4.
Vedantham V, Jethani J, Agarwal A, Vijayalakshmi P. Retinitis pigmentosa associated with blepharophimosis, blue dot cataract and primary inferior oblique overaction: A new syndrome complex?. Indian J Ophthalmol 2007;55:150-1
Smith's recognizable pattern of Human Malformation, Blepharophimosis syndrome. Philadelphia: W.B. Saunders Co; p. 194-5.