CASE REPORT |
|
Year : 2019 | Volume
: 67
| Issue : 1 | Page : 143-145 |
|
Ligneous conjunctivitis in a Dandy–Walker syndrome: A rare case report
Arjun Srirampur1, Muralidhar Ramappa1, Sunita Chaurasia1, Geeta Vemuganti2
1 Department of Cornea and Anterior Segment, Kallam Anji Reddy Campus, Tej Kohli Cornea Institute, LV Prasad Eye Institute, Hyderabad, Telangana, India 2 School of Medicine, Hyderabad University, Hyderabad, Telangana, India
Correspondence Address:
Dr. Muralidhar Ramappa Kallam Anji Reddy Campus, Tej Kohli Cornea Institute, LV Prasad Eye Institute, Banjara Hills, Hyderabad - 560 034, Telangana India
Source of Support: None, Conflict of Interest: None | Check |
DOI: 10.4103/ijo.IJO_772_18
|
|
Ligneous conjunctivitis (LC) is a rare form of pseudomembranous conjunctivitis seen in children, perhaps due to plasminogen deficiency, which manifest as a chronic refractory pseudomembranous conjunctivitis. LC cases are incapable in maintaining their fibrinolytic activity due to plasminogen deficiency; consequently, transudates of plasma assume as a thick, gelatinous, woody membranes over the mucosal surfaces. This is a short case report on a child with a LC, who presented with recurrent pseudomembranous conjunctivitis in conjunction with progressive congenital hydrocephalus due to aqueductal stenosis (Dandy–Walker syndrome). This rare association was clinically confirmed and prompt corrective surgical measures were instituted.
|
|
|
|
[FULL TEXT] [PDF]* |
|
|
|