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   Table of Contents      
OPHTHALMIC IMAGE
Year : 2019  |  Volume : 67  |  Issue : 6  |  Page : 952

Myelinated retinal nerve fibers and persistent hyperplastic primary vitreous


1 Department of Ophthalmology, PGIMER Dr. Ram Manohar Lohia Hospital, New Delhi, India
2 Dr. Rajendra Prasad Centre for Ophthalmic Sciences, All India Institute of Medical Sciences, New Delhi, India

Date of Web Publication24-May-2019

Correspondence Address:
Dr. Vinod Kumar
Dr. Rajendra Prasad Centre for Ophthalmic Sciences, All India Institute of Medical Sciences, New Delhi - 110 029
India
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Source of Support: None, Conflict of Interest: None


DOI: 10.4103/ijo.IJO_1518_18

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How to cite this article:
Gupta S, Shiny H, Bhukya RK, Jain S, Kumar V. Myelinated retinal nerve fibers and persistent hyperplastic primary vitreous. Indian J Ophthalmol 2019;67:952

How to cite this URL:
Gupta S, Shiny H, Bhukya RK, Jain S, Kumar V. Myelinated retinal nerve fibers and persistent hyperplastic primary vitreous. Indian J Ophthalmol [serial online] 2019 [cited 2019 Jun 26];67:952. Available from: http://www.ijo.in/text.asp?2019/67/6/952/259018



A 12-year-old girl presented with decreased vision in OS since early childhood. OD was normal. OS revealed best-corrected visual acuity of hand movements with −9.0 diopters sphere, large exotropia, and posterior subcapsular cataract nasally [Figure 1]a. Fundus [Figure 1]b showed extensive myelinated retinal nerve fibers (MRNFs) and persistent hyperplastic primary vitreous (PHPV) in the form of a fibrous stalk extending from optic disc to lens. Interestingly, while extensive MRNFs are associated with axial myopia, PHPV is associated with a smaller globe.[1],[2],[3] This patient had axial length of 21.84 mm OD and 24.85 mm OS. The parents were apprised of the prognosis. Although both PHPV and MRNF are well-known anomalies in isolation, to the best of our knowledge, combined association of both has not been documented in literature till date. Also, there are very few case reports describing normal/longer axial length in PHPV.[4]
Figure 1: (a) Slit lamp photograph of left eye of a 12-year-old female showing posterior subcapsular cataract nasally. (b) Ultra-wide field pseudo-color photograph showing extensive myelinated nerve fibers and a fibrous stalk (solid arrow) extending between the optic disc and lens (arrow)

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Declaration of patient consent

The authors certify that they have obtained all appropriate patient consent forms. In the form the patient(s) has/have given his/her/their consent for his/her/their images and other clinical information to be reported in the journal. The patients understand that their names and initials will not be published and due efforts will be made to conceal their identity, but anonymity cannot be guaranteed.

Financial support and sponsorship

Nil.

Conflicts of interest

There are no conflicts of interest.



 
  References Top

1.
Goldberg MF. Persistent fetal vasculature (PFV): An integrated interpretation of signs and symptoms associated with persistenthyperplastic primary vitreous (PHPV). LIV Edward Jackson Memorial Lecture. Am J Ophthalmol 1997;124:587-626.  Back to cited text no. 1
    
2.
Haddad R, Font RL, Reeser F. Persistent hyperplastic primary vitreous. A clinicopathologic study of 62 cases and review of the literature. Surv Ophthalmol 1978;23:123-34.  Back to cited text no. 2
    
3.
Tarabishy AB, Alexandrou TJ, Traboulsi EI. Syndrome of myelinated retinal nerve fibers, myopia, and amblyopia: A review. Surv Ophthalmol 2007;52:588-96.  Back to cited text no. 3
    
4.
Trivizki O, Mezad-Koursh D, Stolovich C. Persistent fetal vasculature with atypical presentation. J Ophth Dis 2016;1:105.  Back to cited text no. 4
    


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