|Year : 2019 | Volume
| Issue : 6 | Page : 952
Myelinated retinal nerve fibers and persistent hyperplastic primary vitreous
Sonali Gupta1, Hannah Shiny2, Ravi Kumar Bhukya2, Shreyans Jain2, Vinod Kumar2
1 Department of Ophthalmology, PGIMER Dr. Ram Manohar Lohia Hospital, New Delhi, India
2 Dr. Rajendra Prasad Centre for Ophthalmic Sciences, All India Institute of Medical Sciences, New Delhi, India
|Date of Web Publication||24-May-2019|
Dr. Vinod Kumar
Dr. Rajendra Prasad Centre for Ophthalmic Sciences, All India Institute of Medical Sciences, New Delhi - 110 029
Source of Support: None, Conflict of Interest: None
|How to cite this article:|
Gupta S, Shiny H, Bhukya RK, Jain S, Kumar V. Myelinated retinal nerve fibers and persistent hyperplastic primary vitreous. Indian J Ophthalmol 2019;67:952
|How to cite this URL:|
Gupta S, Shiny H, Bhukya RK, Jain S, Kumar V. Myelinated retinal nerve fibers and persistent hyperplastic primary vitreous. Indian J Ophthalmol [serial online] 2019 [cited 2019 Jun 26];67:952. Available from: http://www.ijo.in/text.asp?2019/67/6/952/259018
A 12-year-old girl presented with decreased vision in OS since early childhood. OD was normal. OS revealed best-corrected visual acuity of hand movements with −9.0 diopters sphere, large exotropia, and posterior subcapsular cataract nasally [Figure 1]a. Fundus [Figure 1]b showed extensive myelinated retinal nerve fibers (MRNFs) and persistent hyperplastic primary vitreous (PHPV) in the form of a fibrous stalk extending from optic disc to lens. Interestingly, while extensive MRNFs are associated with axial myopia, PHPV is associated with a smaller globe.,, This patient had axial length of 21.84 mm OD and 24.85 mm OS. The parents were apprised of the prognosis. Although both PHPV and MRNF are well-known anomalies in isolation, to the best of our knowledge, combined association of both has not been documented in literature till date. Also, there are very few case reports describing normal/longer axial length in PHPV.
|Figure 1: (a) Slit lamp photograph of left eye of a 12-year-old female showing posterior subcapsular cataract nasally. (b) Ultra-wide field pseudo-color photograph showing extensive myelinated nerve fibers and a fibrous stalk (solid arrow) extending between the optic disc and lens (arrow)|
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The authors certify that they have obtained all appropriate patient consent forms. In the form the patient(s) has/have given his/her/their consent for his/her/their images and other clinical information to be reported in the journal. The patients understand that their names and initials will not be published and due efforts will be made to conceal their identity, but anonymity cannot be guaranteed.
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