AU - Srirampur, Arjun AU - Ramappa, Muralidhar AU - Chaurasia, Sunita AU - Vemuganti, Geeta TI - Ligneous conjunctivitis in a Dandy–Walker syndrome: A rare case report PT - CASE DP - 2019 Jan 1 TA - Indian Journal of Ophthalmology PG - 143-145 VI - 67 IP - 1 4099- https://journals.lww.com/ijo/pages/default.aspx/article.asp?issn=0301-4738;year=2019;volume=67;issue=1;spage=143;epage=145;aulast=Srirampur;type=0 4100- https://journals.lww.com/ijo/pages/default.aspx/article.asp?issn=0301-4738;year=2019;volume=67;issue=1;spage=143;epage=145;aulast=Srirampur AB - Ligneous conjunctivitis (LC) is a rare form of pseudomembranous conjunctivitis seen in children, perhaps due to plasminogen deficiency, which manifest as a chronic refractory pseudomembranous conjunctivitis. LC cases are incapable in maintaining their fibrinolytic activity due to plasminogen deficiency; consequently, transudates of plasma assume as a thick, gelatinous, woody membranes over the mucosal surfaces. This is a short case report on a child with a LC, who presented with recurrent pseudomembranous conjunctivitis in conjunction with progressive congenital hydrocephalus due to aqueductal stenosis (Dandy–Walker syndrome). This rare association was clinically confirmed and prompt corrective surgical measures were instituted.