Indian Journal of Ophthalmology

BRIEF COMMUNICATION
Year
: 2017  |  Volume : 65  |  Issue : 9  |  Page : 892--894

Orbital dermatofibrosarcoma protuberans with frontal and ethmoid sinus involvement: A case report and brief review of literature


Deepti Sharma, Garima Singh, Neha Kakkar, Vidya Jha 
 Department of Radiation Oncology, Safdarjung Hospital, New Delhi, India

Correspondence Address:
Deepti Sharma
Room No. 264, Second Floor, New OPD Block, VMMC and Safdarjung Hospital, New Delhi - 110 029
India

Dermatofibrosarcoma protuberans is a soft tissue sarcoma that is dermal in origin. The incidence is <0.1% of all malignancies and 1% of soft tissue sarcoma. Most commonly, it involves trunk (62%) followed by extremities (25%) and head and neck (13%). It is a slow growing tumor with locally aggressive behavior. Here, a 50-year-old female diagnosed with orbital dermatofibrosarcoma developed extra-axial component in right frontal region even on chemotherapy. Hence, the bad prognostic factors are yet to be established in dermatofibrosarcoma protuberans.


How to cite this article:
Sharma D, Singh G, Kakkar N, Jha V. Orbital dermatofibrosarcoma protuberans with frontal and ethmoid sinus involvement: A case report and brief review of literature.Indian J Ophthalmol 2017;65:892-894


How to cite this URL:
Sharma D, Singh G, Kakkar N, Jha V. Orbital dermatofibrosarcoma protuberans with frontal and ethmoid sinus involvement: A case report and brief review of literature. Indian J Ophthalmol [serial online] 2017 [cited 2024 Mar 29 ];65:892-894
Available from: https://journals.lww.com/ijo/pages/default.aspx/article.asp?issn=0301-4738;year=2017;volume=65;issue=9;spage=892;epage=894;aulast=Sharma;type=0