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| CASE REPORT |
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| Year : 1984 | Volume
: 32
| Issue : 4 | Page : 249-250 |
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Congenital cystic eye- a case report
Yogesh Shukla, OP Kulshrestha, Kamal Bajaj
Department of Ophthalmology, S.M.S. Medical College & Hospital Jaipur, India
Correspondence Address:
Yogesh Shukla
Lecturer in Ophthalmology, S.M.S. Medical College & Hospital, Jaipur-302 004
India
 Source of Support: None, Conflict of Interest: None  | Check |
PMID: 6443781 
How to cite this article:
Shukla Y, Kulshrestha O P, Bajaj K. Congenital cystic eye- a case report. Indian J Ophthalmol 1984;32:249-50 |
Congenital cystic eye is a rare anomaly[1],[2]. A partial or complete failure in the involution of the primary optic vesicle results in the formation of a cyst. There is no rudiment of an eye, but only a cyst is present. The cyst may be small or may be quite large, sometimes larger than a normal eye. The cause is unknown and no hereditary tendency has been established.
| Case report | |  |
A small child, aged 8 months came to the out-patients department with the mother giving history of swelling left eye since birth. The swelling was not progressive and non-tender. On examination under general anaesthesia the lids were free from the swelling and a smooth, globular, cyst like swelling was found to replace the eye ball. It was pinkish in color, with no differentiation of sclera and cornea. There was no other abnormality in the vicinity of the eye or elsewhere. The other eye was normal.
| Discussion | | |
After the primary optic vesicle has been formed, instead of the anterior part of the vesicle involuting to lie in opposition with the posterior part so as to leave a merely potential space between the two, a cyst persists and is found to replace the normal eye. The cyst bulges the upper lid, in contra distinction to usual colobomatous cyst which bulges the lower lid. The anterior surface of cyst which forms the inner layers of retina in normal development may sometimes be fairly differentiated but dysplasic, but usually is relatively undifferentiated (as in our case) or is replaced by glia which proliferate to form tumour like masses. The cause, as has been said, is unknown but it is likely that environmental causes are operative[1]. Evidences of inflammatory changes in the wall of the cyst has been sugested'. An alternative theory that failure of mesoderm to invaginate between lens and the margin of the optic cup seems unlikely as has been shown experimentally that the process of invagination is self determining and can occur in vitro when the - vesicle is separated from its surrounding tissues[2].
| Summary | | |
A case of unilateral congenital cystic eye is presented. The anomaly is a rare one. Although cases have been reported, no definite cause of its occurence is known.
| References | | |
| 1. | Duke-Elder, S., 1964, . System of Ophthalmology, Vol. III Part II Normal & abnormal development. Henry Kimpton, London.  |
| 2. | Sorsby, A., 1972, Modern Ophthalmology. 2nd Ed. Vol. 3. Topical aspects. Butterworths, London. |
[Figure - 1]
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