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Year : 1984  |  Volume : 32  |  Issue : 4  |  Page : 249-250

Congenital cystic eye- a case report

Department of Ophthalmology, S.M.S. Medical College & Hospital Jaipur, India

Correspondence Address:
Yogesh Shukla
Lecturer in Ophthalmology, S.M.S. Medical College & Hospital, Jaipur-302 004
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Source of Support: None, Conflict of Interest: None

PMID: 6443781

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How to cite this article:
Shukla Y, Kulshrestha O P, Bajaj K. Congenital cystic eye- a case report. Indian J Ophthalmol 1984;32:249-50

How to cite this URL:
Shukla Y, Kulshrestha O P, Bajaj K. Congenital cystic eye- a case report. Indian J Ophthalmol [serial online] 1984 [cited 2023 Feb 1];32:249-50. Available from: https://www.ijo.in/text.asp?1984/32/4/249/27402

Congenital cystic eye is a rare anomaly[1],[2]. A partial or complete failure in the involution of the primary optic vesicle results in the forma­tion of a cyst. There is no rudiment of an eye, but only a cyst is present. The cyst may be small or may be quite large, sometimes larger than a normal eye. The cause is unknown and no hereditary tendency has been established.

  Case report Top

A small child, aged 8 months came to the out-patients department with the mother giv­ing history of swelling left eye since birth. The swelling was not progressive and non-tender. On examination under general anaesthesia the lids were free from the swelling and a smooth, globular, cyst like swelling was found to replace the eye ball. It was pinkish in color, with no differentiation of sclera and cornea. There was no other abnormality in the vicinity of the eye or elsewhere. The other eye was normal.

  Discussion Top

After the primary optic vesicle has been formed, instead of the anterior part of the vesi­cle involuting to lie in opposition with the posterior part so as to leave a merely potential space between the two, a cyst persists and is found to replace the normal eye. The cyst bulges the upper lid, in contra distinction to usual colobomatous cyst which bulges the lower lid. The anterior surface of cyst which forms the inner layers of retina in normal development may sometimes be fairly dif­ferentiated but dysplasic, but usually is relatively undifferentiated (as in our case) or is replaced by glia which proliferate to form tumour like masses. The cause, as has been said, is unknown but it is likely that environ­mental causes are operative[1]. Evidences of inflammatory changes in the wall of the cyst has been sugested'. An alternative theory that failure of mesoderm to invaginate between lens and the margin of the optic cup seems unlikely as has been shown experimentally that the process of invagination is self determining and can occur in vitro when the - vesicle is separated from its surrounding tissues[2].

  Summary Top

A case of unilateral congenital cystic eye is presented. The anomaly is a rare one. Although cases have been reported, no definite cause of its occurence is known.

  References Top

Duke-Elder, S., 1964, . System of Ophthalmology, Vol. III Part II Normal & abnormal development. Henry Kimpton, London.  Back to cited text no. 1
Sorsby, A., 1972, Modern Ophthalmology. 2nd Ed. Vol. 3. Topical aspects. Butterworths, London.  Back to cited text no. 2


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