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OPHTHALMIC IMAGES
Year : 2018  |  Volume : 66  |  Issue : 3  |  Page : 450

Acorea: A rare congenital anomaly


1 Department of Pediatric Ophthalmology, Sankara Nethralaya, Chennai, Tamil Nadu, India
2 Department of Uvea, Sankara Nethralaya, Chennai, Tamil Nadu, India

Date of Web Publication26-Feb-2018

Correspondence Address:
Dr. Srikanth Ramasubramanian
Department of Pediatric Ophthalmology, Sankara Nethralaya, No. 41 (old 18), College Road Chennai - 600 006, Tamil Nadu
India
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Source of Support: None, Conflict of Interest: None


DOI: 10.4103/ijo.IJO_900_17

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How to cite this article:
Ramasubramanian S, Majumder PD. Acorea: A rare congenital anomaly. Indian J Ophthalmol 2018;66:450

How to cite this URL:
Ramasubramanian S, Majumder PD. Acorea: A rare congenital anomaly. Indian J Ophthalmol [serial online] 2018 [cited 2024 Mar 28];66:450. Available from: https://journals.lww.com/ijo/pages/default.aspx/text.asp?2018/66/3/450/226126



A young male presented to our clinic with a history of diminution of vision in the left eye from childhood. His vision in the left eye was hand movement at 1 M distance. Slit-lamp examination of the left eye showed the absence of pupillary opening with folds of iris tissue at center [Figure 1]a. Krimsky test measured 35 prism diopter of exotropia. No family history of similar condition was noted. Lens status and ultrasonography B-scan of the left eye was within normal limit. Anterior segment optical coherence tomography revealed an open-angle and absence of pupillary opening [Figure 1]b. A diagnosis of acorea was made. Acorea can be associated with microphthalmos, cataract, and iridocorneal dysgenesis which is suspected to result from autosomal dominant mutation. If diagnosed early, a pupilloplasty can help prevent the development of stimulus deprivation amblyopia.
Figure 1: (a) Slit-lamp photograph of the left eye showing the absence of pupil with folds of iris tissue at the center. (b) Anterior segment optical coherence tomography of the left eye showing the absence of pupil

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Declaration of patient consent

The authors certify that they have obtained all appropriate patient consent forms. In the form the patient(s) has/have given his/her/their consent for his/her/their images and other clinical information to be reported in the journal. The patients understand that their names and initials will not be published and due efforts will be made to conceal their identity, but anonymity cannot be guaranteed.

Financial support and sponsorship

Nil.

Conflicts of interest

There are no conflicts of interest.




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