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Year : 2020  |  Volume : 68  |  Issue : 10  |  Page : 2243-2244

A rare case of bilateral congenital upper eyelid eversion managed conservatively

1 Department of Eye, BJ Hospital and Research Institute Pvt. Ltd., Gondia, Maharashtra, India
2 Department of Paediatric, BJ Hospital and Research Institute Pvt. Ltd., Gondia, Maharashtra, India

Date of Submission07-Jan-2020
Date of Acceptance24-Mar-2020
Date of Web Publication23-Sep-2020

Correspondence Address:
Nilesh Jain
Department of Eye, BJ Hospital and Research Institute Pvt. Ltd., Ganesh Nagar, Gondia, Maharashtra - 441 601
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Source of Support: None, Conflict of Interest: None

DOI: 10.4103/ijo.IJO_35_20

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Keywords: Bilateral, eversion, hypertonic saline, upper eyelid

How to cite this article:
Jain N, Jain J. A rare case of bilateral congenital upper eyelid eversion managed conservatively. Indian J Ophthalmol 2020;68:2243-4

How to cite this URL:
Jain N, Jain J. A rare case of bilateral congenital upper eyelid eversion managed conservatively. Indian J Ophthalmol [serial online] 2020 [cited 2022 Aug 7];68:2243-4. Available from: https://www.ijo.in/text.asp?2020/68/10/2243/295736

A 12-h-old female infant was referred to our tertiary care hospital from another hospital for the management of eversion of both upper eyelids. The full-term neonate was born by cesarean section for failed induction of labor. On ocular examination, her upper eyelids were totally everted (left eye more than the right eye) with severe conjunctival chemosis and greenish discharge suggestive of secondary infection [Figure 1]. After instillation of 0.5% proparacaine eye drops and using Desmarre's lid retractor, the anterior segment was examined which was normal with negative fluorescein staining of the cornea. On laboratory testing, the neonate had C- reactive proteins (CRP) level of 5.1 mg/dL. Elevated total leukocyte count (17,000/μL) with raised total (10.2 mg/dL) and indirect bilirubin (9.46 mg/dL) levels. The neonate was admitted to the neonatal intensive care unit (NICU) for neonatal sepsis and hyperbilirubinemia. The baby was started on systemic antibiotics and phototherapy. For ocular pathology, manual eversion was tried without any success. After that, magnesium sulfate soaked dressings were given to reduce chemosis but there was no positive response. So, we tried 5% hypertonic NaCl soaked dressings every 6 h. This resulted in a reduction in chemosis from day 2 and on day 6 the chemosis was completely reduced with normal closure of the eyelid [Figure 2]. Along with this, the neonate was also given 0.5% moxifloxacin eye drops and topical 1% carboxyl methylcellulose (CMC) eyedrops every 6 h.
Figure 1: At the time of presentation

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Figrue 2: At day 6

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  Discussion Top

Bilateral congenital upper eyelid eversion is a rare disorder. Adams, in 1896, first described congenital eversion of both eyelid as “ double congenital ectropion.”[1] In 1992, Sellar reported 51 cases after reviewing the literature.[2] 7 more cases reported till now.[3],[4],[5],[6],[7] This is seen frequently in infants with Down syndrome, collodion skin disease, and Black race.

The presentation of the disease can be unilateral or bilateral. The exact etiopathogenesis is not known but multiple theories have been proposed to describe its etiology. This includes birth trauma, hypotonia of orbicularis oculi muscle, anterior lamellar shortening and posterior lamellar widening of the eyelid, failure of the orbital septum and levator aponeurosis fusion, elongation of eyelid laterally, and inelastic lateral canthal ligament.[5] The orbicularis spasm leads to venous stasis and conjunctival chemosis thus preventing the cornea from infection and exposure.[8]

In conservative management, various treatment modalities available which include moist dressing, taping of the eyelid, pressure patching, hypertonic saline dressing, topical antibiotics, and lubricants.[8],[9]

The surgical management options include scarification of exposed conjunctiva, temporary tarsorrhaphy, subconjunctival injection of hyaluronic acid, fornix sutures, and full-thickness upper lid skin graft.[5],[9],[10] But these are used in cases not responding to conservative treatment. Also, lid manipulations can lead to stimulation of autonomic effects such as respiratory arrest in neonates.[3]

Our case was managed with hypertonic saline dressing, antibiotic and lubricating eyedrops. Early treatment can prevent complications like conjunctival scarring, epimerization, and secondary infection. This case report advocates the need for a strictly conservative approach in management.

The aim of this photo essay is to create awareness among those who are first-time viewers like health care professionals in ophthalmology and neonatology.

Declaration of patient consent

The authors certify that they have obtained all appropriate patient consent forms. In the form the patient(s) has/have given his/her/their consent for his/her/their images and other clinical information to be reported in the journal. The patients understand that their names and initials will not be published and due efforts will be made to conceal their identity, but anonymity cannot be guaranteed.

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Conflicts of interest

There are no conflicts of interest.

  References Top

Adams AL. A case of double congenital ectropion. Med Forthnightly 1896;9:137-8.  Back to cited text no. 1
Sellar PW, Bryars JH, Archer DB. Late presentation of congenital ectropion of the eyelids in a child with Downs's syndrome: A case report and review of the literature. J Pediatr Ophthalmol Strabismus 1992;29:64-7.  Back to cited text no. 2
Watts MT, Dapling RB. Congenital eversion of the upper eyelid: A case report. Ophthal Plast Reconstr Surg 1995;11:293-5.  Back to cited text no. 3
Dawodu OA. Total eversion of the upper eyelids in a newborn. Niger Postgrad Med J 2001;8:145-7.  Back to cited text no. 4
  [Full text]  
Al Hussain HA, Al-Rajhi AA, Al-Qahtani S, Meyer D. Congenital upper eyelid eversion complicated by corneal perforation. Br J Ophthalmol 2005;89:771.  Back to cited text no. 5
Maheshwari R, Maheshwari S. Congenital eversion of upper eyelids: Case report and management. Indian J Ophthalmol 2006;54:203-4.  Back to cited text no. 6
[PUBMED]  [Full text]  
Dohvoma VA, Nchifor A, Ngwanou AN, Attha E, Ngounou F, Bella AL, et al. Conservative management in congenital bilateral upper eyelid eversion. Case Rep Ophthalmol Med 2015;2015:389289.  Back to cited text no. 7
Adeoti CO, Ashaye AO, Isawumi MA, Raji RA. Non-surgical management of congenital eversion of the eyelids. J Ophthalmic Vis Res 2010;5:188-92.  Back to cited text no. 8
  [Full text]  
Devika P, Bhagavan V, Rao DD, Hegde S, Kotian VB. Case report of bilateral congenital upper eyelid eversion in a newborn. Res Rev: J Med Health Sci 2014;3:22-4.  Back to cited text no. 9
Fasina O. Management of bilateral congenital upper eyelid eversion with severe chemosis. J Ophthalmic Vis Res 2013;8:175-8.  Back to cited text no. 10
  [Full text]  


  [Figure 1], [Figure 2]

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