CASE REPORT |
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Year : 2020 | Volume
: 68
| Issue : 11 | Page : 2615-2617 |
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Combined medical and surgical management for cicatricial ectropion in lamellar ichthyosis: A report of three cases
Nirmala Subramanian1, Pratheeba Devi Nivean2, Md Shahid Alam3
1 Department of Orbit Oculoplasty and Reconstructive Surgery, Medical Research Foundation, Chennai, Tamil Nadu, India 2 Department of Oculoplasty, M N Eye Hospital, Chennai, Tamil Nadu, India 3 Orbit Oculoplasty Reconstructive and Aesthetic Services, Aditya Birla Sankara Nethralaya, (A Unit of Medical Research Foundation, Chennai), Kolkata, West Bengal, India
Correspondence Address:
Dr. Pratheeba Devi Nivean Department of Oculoplasty, M N Eye Hospital, Chennai, Tamil Nadu India
Source of Support: None, Conflict of Interest: None | Check |
DOI: 10.4103/ijo.IJO_855_20
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Ichthyosis is a rare inherited skin disorder characterized by abnormal keratinization of the epidermis. Cicatricial ectropion is the most common ophthalmic feature of congenital ichthyosis. Progressive subepithelial cicatrization and abnormal cornification of eyelid skin cause progressive ectropion in both eyelids, leading to lagophthalmos and corneal exposure. Surgical correction of cicatricial ectropion in these cases is challenging with unsatisfactory results. Proper processing of the donor and recipient site with lubricants and topical retinoids before surgery makes grafting easier and its survival better. We present three cases of lamellar ichthyosis with cicatricial ectropion managed with combined preoperative topical therapy followed by surgery. All patients had extremely good surgical outcomes, with none of them requiring repeat surgery.
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